Literature associating GCDH and L-2-hydroxyglutaric aciduria
GCDH [ENSP00000222214]
Glutaryl-CoA dehydrogenase, mitochondrial; Catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and CO(2) in the degradative pathway of L-lysine, L-hydroxylysine, and L-tryptophan metabolism. It uses electron transfer flavoprotein as its electron acceptor. Isoform Short is inactive; Belongs to the acyl-CoA dehydrogenase family.
Synonyms: GCDH, A0A024R7F9, GCDH-001, GCDH-002, GCDH-003 ...