DISEASES

Disease-gene associations mined from literature

Human genes for progressive familial intrahepatic cholestasis 5

Progressive familial intrahepatic cholestasis 5 [DOID:0070225]

A progressive familial intrahepatic cholestasis characterized by autosomal recessive inheritance of intralobular cholestasis with onset in the neonatal period that has_material_basis_in mutation in the NR1H4 gene on chromosome 12q.

Synonyms:  progressive familial intrahepatic cholestasis 5,  DOID:0070225,  progressive hereditary intrahepatic cholestasis 5,  NR1H4 deficiency,  PFIC5