DISEASES

Disease-gene associations mined from literature

Human genes for microcephalic osteodysplastic primordial dwarfism type I

Microcephalic osteodysplastic primordial dwarfism type I [DOID:0060608]

A microcephalic osteodysplastic primordial dwarfism that is characterized by dwarfism, microcephaly, mental retardation, brain malformations, and ocular, auditory sensory deficits and that has_material_basis_in homozygous or compound heterozygous mutation in the RNU4ATAC gene, encoding a small nuclear RNA component of the U12-dependent spliceosome, on chromosome 2q14.2.

Synonyms:  microcephalic osteodysplastic primordial dwarfism type I,  DOID:0060608,  microcephalic osteodysplastic primordial dwarfism type Is,  brachymelic primordial dwarfism,  cephaloskeletal dysplasia ...