Literature on ECHDC1
ECHDC1 [ENSP00000436585]
Ethylmalonyl-CoA decarboxylase; Decarboxylates ethylmalonyl-CoA, a potentially toxic metabolite, to form butyryl-CoA, suggesting it might be involved in metabolite proofreading . Also has methylmalonyl-CoA decarboxylase activity at lower level (By similarity).
Synonyms: ECHDC1, ECHDC1p, hECHDC1, E9PIU8, E9PJS8 ...