Literature associating HIBCH and mitochondrial metabolism disease
HIBCH [ENSP00000352706]
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial; Hydrolyzes 3-hydroxyisobutyryl-CoA (HIBYL-CoA), a saline catabolite. Has high activity toward isobutyryl-CoA. Could be an isobutyryl-CoA dehydrogenase that functions in valine catabolism. Also hydrolyzes 3-hydroxypropanoyl-CoA.
Synonyms: HIBCH, A0A140VJL0, B8ZZZ0, B9A058, F8W8A6 ...